You are here

Home » Islandora Repository » Western Sydney University Research Collection
My bookmarks

The international WAO/EAACI guideline for the management of hereditary angioedema : the 2021 revision and update

Search for this publication on Google Scholar
Maurer, M., Magerl, M., Betschel, S., Aberer, W., Ansotegui, I., Aygoren-Pursun, E., … Craig, T. (2022). The international WAO/EAACI guideline for the management of hereditary angioedema : the 2021 revision and update. World Allergy Organization Journal, 15(3). https://doi.org/10.1016/j.waojou.2022.100627
Download PDF

Abstract

Hereditary Angioedema (HAE) is a rare and disabling disease for which early diagnosis and effective therapy are critical. This revision and update of the global WAO/EAACI guideline on the diagnosis and management of HAE provides up-to-date guidance for the management of HAE. For this update and revision of the guideline, an international panel of experts reviewed the existing evidence, developed 28 recommendations, and established consensus by an online DELPHI process. The goal of these recommendations and guideline is to help physicians and their patients in making rational decisions in the management of HAE with deficient C1-inhibitor (type 1) and HAE with dysfunctional C1-inhibitor (type 2), by providing guidance on common and important clinical issues, such as: 1) How should HAE be diagnosed? 2) When should HAE patients receive prophylactic on top of on-demand treatment and what treatments should be used? 3) What are the goals of treatment? 4) Should HAE management be different for special HAE patient groups such as children or pregnant/breast feeding women? 5) How should HAE patients monitor their disease activity, impact, and control? It is also the intention of this guideline to help establish global standards for the management of HAE and to encourage and facilitate the use of recommended diagnostics and therapies for all patients.

 0 Views  6 Downloads
Details
Title
The international WAO/EAACI guideline for the management of hereditary angioedema : the 2021 revision and update
Language
eng
Date
2022
Author
Maurer, Marcus                
Magerl, Markus                
Betschel, Stephen             
Aberer, Werner                
Ansotegui, Ignacio            
Aygoren-Pursun, Emel          
Banerji, Aleena               
Bara, Noemi-Anna              
Boccon-Gibod, Isabelle        
Bork, Konrad                  
Show 49 more
Extent
39
DOI
10.1016/j.waojou.2022.100627
Scopus_ID
2-s2.0-85127772980
Handle
https://hdl.handle.net/1959.7/uws:70385
URL
https://doi.org/10.1016/j.waojou.2022.100627
Publication Type
journal article
Copyright
© 2022 The Author(s). Published by Elsevier Inc. on behalf of World Allergy Organization. This is an open access article under the CC BYNC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
Relation
World Allergy Organization Journal
ISSN
1939-4551
Volume, Issue, Pages
Vol. 15, Issue 3, No. 100627
Volume
15
Issue
3
Number
100627
Publisher
Elsevier
Place Published
Netherlands